The absence of an enzyme that is involved in the catabolism of lipids results in:

Explanation

In Tay-Sachs disease, lipid storage refers to the abnormal accumulation of a specific lipid within the nerve cells of the brain andspinal cord. The accumulation of the lipid occurs due to a deficiency or complete absence of a specific enzyme called hexosaminidase A (Hex-A). This enzyme is responsible for breaking down the complex substance into simpler components that can be recycled or eliminated from the cells. In individuals with Tay-Sachs disease, mutations in the gene lead to the defective production of the enzyme. As a result, the lipid cannot be broken down properly and starts to accumulate within the lysosomes, which are cellular structures responsible for breaking down various substances.