Moderate
In maple syrup urine disease the amino acids excreted in the urine are______________?
Correct answer: D. All of the above
- A. Leucine
- B. Isoleucine
- C. Valine
- D. All of the above
Explanation
Maple syrup urine disease results from deficiency of the branched-chain alpha-ketoacid dehydrogenase complex, causing leucine, isoleucine and valine to accumulate and be excreted. Therefore, all three listed amino acids are involved.
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